About Sickle Cell

Sickle cell disease (SCD) represents a group of inherited disorders that impact haemoglobin, the protein found in red blood cells that is essential for oxygen transport throughout the body. In individuals diagnosed with SCD, the haemoglobin is altered, resulting in red blood cells that become rigid, sticky, and assume a crescent or "sickle" shape. This abnormal morphology can lead to obstructions in small blood vessels, thereby hindering the proper flow of blood and the delivery of oxygen to various tissues and organs. This is referred to as a crisis, as it causes significant pain. 

All children with sickle cell disease require a care plan when they start nursery. Please inform us when your child begins nursery, and we will create a care plan for you. Once it is prepared, we will send it to you for your review. We kindly request that you read, edit, sign, and return the document to us. We will then provide copies to you and the nursery. Care plans are updated annually. Additionally, the nursery staff will receive training on how to care for a child with sickle cell disease. This same process will apply when your child starts school.

Triggers

  • Sudden changes in weather
  • Dehydration
  • Infection
  • High Altitude
  • Extreme Cold
  • Extreme Hot weather
  • Overexertion
  • Alcohol
  • Smoking
  • Swimming

Medications

Penicillin Prophylaxis

Penicillin V should be offered to all children according to the following dosage schedule:

  • 125mg po bd from 3 months -5yr
  • 250mg po bd >5yr

Erythromycin is a suitable alternative if a documented penicillin allergy is present.

Folic acid-2.5mg from 3 months and 5mg at age 5

Immunisations

Sickle cell vaccine chart